I-Retinitis Pigmentosa

I-Retinitis Pigmentosa

Yintoni iRetinitis Pigmentosa?

Ukupapashwa kwezeMpilo eHarvard

I-Retinitis pigmentosa (RP) sisifo samehlo. Kukhokelela ekuphulukaneni nombono ngokuthe ngcembe kwaye, ngamanye amaxesha, ukungaboni.

I-RP yenzeka xa iiseli zokujonga ukukhanya kwiliso zihla. Ezi seli, zibizwa ngokuba ziirandi kunye neekhowuni, zibekwe kwiretina. Le yinxalenye yangasemva yamehlo efumana ukukhanya okuza kwiliso, kwaye ithumela olo lwazi lubonakalayo kwingqondo.

Iimpawu ze-RP zihlala ziqala ebudaleni, nangona zinokuqala kubuntwana. Uninzi lwabantu abane-RP ngokusemthethweni aluboni kangangeminyaka engama-40, nangona besenombono othile. Inani elipheleleyo lokulahleka kombono kunye nokukhawuleza kwesi sifo sihluka ukusuka kumntu ukuya kumntu.



Akukho mntu waziyo kanye ukuba yintoni ebangela i-RP. Kukholelwa ukuba sisifo esizuzwe njengelifa. Nangona kunjalo, kwezinye iimeko, esi sifo sivela kubantu abangenayo imbali yosapho yesi sifo.

I-medrol dosepak 4 mg ithebhulethi yomlomo

Ukuphazamiseka nako kunokubonisa njengenxalenye yamanye ama-syndromes. Oku kubandakanya isifo seBassen-Kornzweig okanye isifo seKearns-Sayre.

Iimpawu

Iimpawu zokuqala ze-RP zihlala zinciphisa umbono wobusuku. Kuya kusiba nzima ngakumbi ukubona kwiindawo ezikhanyayo okanye ezimnyama.

Abantu abane-RP nabo baphulukana ngokuthe ngcembe nombono (wecala) kunye nokubukhali okubonakalayo.

Ixesha elingaphezulu, ukuphazamiseka kukhokelela kumbono wetonela. Imiphetho engaphandle yombono imnyama, ishiya isangqa esinciphayo sombono embindini.

Ekugqibeleni, abantu abane-RP banokungaboni. Kodwa uninzi lwabantu abanale ngxaki bagcina umbono othile, naxa sele bekhulile.

Uxilongo

Uya kufunyaniswa ngugqirha wamehlo. Lo ngugqirha ogxile kukuphazamiseka kwamehlo.

Ugqirha wamehlo angenza inani leemvavanyo zokuqonda isifo. Ugqirha uya kusebenzisa isixhobo esibizwa ngokuba yi-ophthalmoscope ukujonga ngaphakathi kweliso ngomfundi. Kwiliso eliqhelekileyo, ugqirha uza kubona indawo ebomvu okanye eorenji ebomvu ebizwa ngokuba yingxowa-mali. Kumntu one-RP, indawo yeorenji iya kuba neblack brown okanye emnyama.

Uvavanyo lwentsimi ebonakalayo lunokwenziwa. Le milinganiselo yombono womntu.

Ukuqinisekisa ukuxilongwa kwe-retinitis pigmentosa, i-ophthalmologist ingenza i-electroretinogram (ERG). Ngexesha lovavanyo, ukukhanya kwemibala eyahlukeneyo kunye nokuqina kuyakhanya kwiso lakho njengoko ujonge kumhlaba omkhulu obonakalisayo. Iilensi zonxibelelwano eziqulethe i-electrode zibekwe kwiliso lakho. Ucingo ludlulisa irekhodi lomsebenzi we-retina. I-ERG idala iphepha lokujonga iimpembelelo zombane. Abantu abane-RP banemisebenzi yombane esezantsi kunesiqhelo kwiretina yabo.

Ixesha elilindelekileyo

RP rhoqo kukuphazamiseka kwilifa.

Oogqirha abenza uvavanyo lwamehlo banokubona imiqondiso yokuqala ye-RP kwasekuqaleni kweminyaka ye-10. Iimpawu zihlala ziqala ebusheni okanye ebudaleni. Bacotha kancinci ekuhambeni kwexesha.

Ubukhulu besifo buyahluka kuye ngomntu. Nangona kunjalo, ukungahambi kakuhle kunye nokulahleka kokubonakalayo kuhlala kubomi bonke.

Uthintelo

Ngenxa yokuba i-RP kukuphazamiseka kwemfuza, akukho ndlela yakukuthintela oko. Akukho ndlela iqinisekisiweyo yokuthintela okanye yokulibazisa ukulahleka kombono okuhambelana noko.

Unyango

Akukho lonyango lwaziwayo lwe-RP.

Ixabiso le percocet 5/325

Olunye uphando lubonisa ukuba iidosi eziphezulu zevithamini A (15,000 IU / ngosuku) zinokucothisa ukonakala kancinci kwabanye abantu. Nangona kunjalo, ubungqina boku abunamandla. Ukongeza, kunokubakho iziphumo ezinetyhefu yokuthatha ivithamin A.

Ukuba unayo i-RP kwaye ufuna ukuzama unyango lwe-vitamin A, thetha nogqirha wakho kuqala. Buza malunga nokhuseleko kunye nexabiso elinokubakho lonyango.

Ezinye izigulana ezine-RP ziphuhlisa i-macular edema. Ukuqokelelwa kolwelo kumbindi wamehlo kunokukhawulezisa ukulahleka kombono. Oku kunokunyangwa nge-carbonic anhydrase inhibitor kwifomu yomlomo okanye njengamathontsi wamehlo. Isiyobisi esisetyenziswa ngokuqhelekileyo yi-acetazolamide.

iivith d 50000 iu d2

Nini ukubiza iNgcali

Jonga umsebenzi wakho wokhathalelo lwempilo ukuba ubona naluphi na utshintsho kumbono wakho. Oku kubandakanya ukunciphisa ukubanakho ukubona ebusuku okanye ukulahleka kombono womda.

Ukuxela kwangaphambili

RP ayinakunyangeka. Ilahleko ebonakalayo iyaqhubeka kwaye isigxina.

Isixa kunye nesantya sokonakala kuyahluka ngokwamntu. Ke ngoko, ubungakanani bokulahleka kombono akunakuqikelelwa.

Izigulana ezininzi ezinengxaki yale meko zikhokelela kubomi obuqhelekileyo.

Izixhobo zangaphandle

IAmerican Academy yeOphthalmology
http://www.aao.org/

IZiko leLiso leSizwe
http://www.nei.nih.gov/

Inkcukacha ezithe vetshe

Njalo qhagamshelana nomboneleli wakho wezempilo ukuqinisekisa ukuba ulwazi oluboniswe kweli phepha lisebenza kwiimeko zakho zobuqu.

Ukuzihlangula kwezonyango